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产品信息
PA5-142618
产品规格
种属反应
Rat
宿主/亚型
Goat
/ IgG
分类
Polyclonal
类型
Antibody
抗原
Peptide with sequence C-TTGNYRIESVLS.
偶联物
形式
Liquid
浓度
0.5 mg/mL
纯化类型
Ammonium sulfate precipitation
保存液
TBS, pH 7.3, with 0.5% BSA
内含物
0.02% sodium azide
保存条件
-20° C, Avoid Freeze/Thaw Cycles
运输条件
Wet ice
RRID
AB_2933264
产品详细信息
Additional Information: This antibody is expected to recognize isoform 1 (NP_000396.2) only.
This antibody is tested in Peptide ELISA: antibody detection limit dilution 1:4,000.
靶标信息
This gene encodes a small glycolipid transport protein which acts as a substrate specific co-factor for the lysosomal enzyme beta-hexosaminidase A. Beta-hexosaminidase A, together with GM2 ganglioside activator, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Mutations in this gene result in GM2-gangliosidosis type AB or the AB variant of Tay-Sachs disease. Alternative splicing results in multiple transcript variants.
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生物信息学
蛋白别名: ganglioside GM2 activator; GM2 ganglioside activator protein
Entrez Gene ID: (Rat) 282838
ganglioside metabolic process
ganglioside catabolic process
lipid transport
learning or memory
oligosaccharide catabolic process
lipid storage
positive regulation of catalytic activity
neurological system process
neuromuscular process controlling balance
positive regulation of hydrolase activity
membrane fusion
