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产品信息
PA5-120202
应用
建议稀释比
已发表文章
产品规格
宿主/亚型
Rabbit
/ IgG
分类
Polyclonal
类型
Antibody
抗原
Recombinant fusion protein containing a sequence corresponding to amino acids 484-763 of human HADHA (NP_000173.2).
偶联物
形式
Liquid
浓度
1.89 mg/mL
保存条件
-20° C, Avoid Freeze/Thaw Cycles
运输条件
Wet ice
RRID
AB_2913774
产品详细信息
Positive test controls include: 293T, K-562. The target is usually found in the following locations: Mitochondrion.
Immunogen sequence: IAAVSKRPEK VIGMHYFSPV DKMQLLEIIT TEKTSKDTSA SAVAVGLKQG KVIIVVKDGP GFYTTRCLAP MMSEVIRILQ EGVDPKKLDS LTTSFGFPVG AATLVDEVGV DVAKHVAEDL GKVFGERFGG GNPELLTQMV SKGFLGRKSG KGFYIYQEGV KRKDLNSDMD SILASLKLPP KSEVSSDEDI QFRLVTRFVN EAVMCLQEGI LATPAEGDIG AVFGLGFPPC LGGPFRFVDL YGAQKIVDRL KKYEAAYGKQ FTPCQLLADH ANSPNKKFYQ
靶标信息
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
仅用于科研。不用于诊断过程。未经明确授权不得转售。
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