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SGSH Antibody (PA5-96950) in WB
Western blot analysis of SGSH in mouse lung. Samples were incubated with SGSH Polyclonal antibody (Product # PA5-96950) using a dilution of 1:500, followed by HRP Goat Anti-Rabbit IgG (H+L) at a dilution of 1:10,000. Lysates/proteins: 25 µg per lane. Blocking buffer: 3% nonfat dry milk in TBST. Detection: ECL Basic Kit. Exposure time: 90s.
产品信息
PA5-96950
产品规格
种属反应
Human,
Mouse,
Rat
宿主/亚型
Rabbit
/ IgG
分类
Polyclonal
类型
Antibody
抗原
Recombinant fusion protein containing a sequence corresponding to amino acids 273-502 of human SGSH (NP_0001901)
偶联物
形式
Liquid
浓度
0.79 mg/mL
纯化类型
Affinity Chromatography
保存液
PBS, pH 7.3, with 50% glycerol
内含物
0.02% sodium azide
保存条件
-20° C, Avoid Freeze/Thaw Cycles
运输条件
Wet ice
RRID
AB_2808752
产品详细信息
Immunogen sequence: DNGIPFPSGR TNLYWPGTAE PLLVSSPEHP KRWGQVSEAY VSLLDLTPTI LDWFSIPYPS YAIFGSKTIH LTGRSLLPAL EAEPLWATVF GSQSHHEVTM SYPMRSVQHR HFRLVHNLNF KMPFPIDQDF YVSPTFQDLL NRTTAGQPTG WYKDLRHYYY RARWELYDRS RDPHETQNLA TDPRFAQLLE MLRDQLAKWQ WETHDPWVCA PDGVLEEKLS PQCQPLHNEL; Positive Samples: MCF7, 22Rv1, HepG2, Mouse liver, Mouse testis; Cellular Location: Lysosome
靶标信息
SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
仅用于科研。不用于诊断过程。未经明确授权不得转售。
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生物信息学
蛋白别名: heparan sulfate sulfatase; mucopolysaccharidosis type IIIA; N-sulfoglucosamine sulfohydrolase; N-sulphoglucosamine sulphohydrolase; Sulfoglucosamine sulfamidase; Sulphamidase
基因别名: 4632406A19Rik; HSS; MPS3A; SFMD; SGSH
UniProt ID: (Human) P51688
Entrez Gene ID: (Human) 6448, (Rat) 688293, (Mouse) 27029
